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Alveolar capillary dysplasia, although rare, is a universally fatal form of persistent pulmonary hypertension of the newborn. We report a case of a newborn male baby who developed respiratory distress and pneumothorax 11 h after an uncomplicated delivery. He deteriorated despite full ventilatory support and extracorporeal membrane oxygenation (ECMO). Open lung biopsy provided a diagnosis of alveolar capillary dysplasia and decision was made to withdraw treatment.

Original publication




Journal article


Pediatr Surg Int

Publication Date





915 - 917


Biopsy, Capillaries, Diagnosis, Differential, Extracorporeal Membrane Oxygenation, Fatal Outcome, Humans, Infant, Newborn, Lung, Male, Persistent Fetal Circulation Syndrome, Pneumothorax, Pulmonary Alveoli, Rare Diseases, Respiration, Artificial, Respiratory Distress Syndrome, Newborn